ABSTRACT
We report a rare case of non-communicating large orbital cyst with microphthalmos which was surgically separated from the globe and excised. Histopathology reported it to be a teratoma. Congenital cystic teratoma should be a part of the differential diagnosis in an infant presenting with a clinical picture of microphthalmos with orbital cyst, in view of the different management required.
Subject(s)
Cysts/diagnosis , Diagnosis, Differential , Female , Humans , Infant , Microphthalmos/diagnosis , Ophthalmologic Surgical Procedures/methods , Orbital Neoplasms/congenital , Orbital Neoplasms/diagnosis , Orbital Neoplasms/surgery , Teratoma/congenital , Teratoma/diagnosis , Teratoma/surgery , Tomography, X-Ray ComputedABSTRACT
Apresentamos um caso de tumor orbitário congênito de grande tamanho, ocorrendo em criança recém-nascida. A paciente foi submetida a exenteração da órbita e o diagnóstico anatomopatológico foi de teratoma cístico. Os aspectos clínico-patológicos desta rara doença são comentados.
We report on a case of an congenital orbital tumor of impressive size, occurring in a newborn. The patient underwent orbital exenteration with a histopathologic diagnosis of cystic teratoma. The clinicopathological aspects of such a rare disease are commented.
Subject(s)
Female , Humans , Infant, Newborn , Orbital Neoplasms/pathology , Teratoma/pathology , Orbit Evisceration , Orbital Neoplasms/congenital , Orbital Neoplasms/surgery , Teratoma/congenital , Teratoma/surgeryABSTRACT
Microftalmia com cisto colobomatoso orbitário é raro diagnóstico diferencial dos tumores congênitos orbitários. O diagnóstico precoce e o tratamento adequado são importantes para bom crescimento órbito-palpebral. Descrevemos três casos de microftalmia congênita associada a cisto colobomatoso orbitário e analisamos a importância dos exames complementares. Ultra-sonografia, tomografia computadorizada, ressonância nuclear magnética e o estudo histológico da massa excisada estabeleceram o diagnóstico preciso de cisto colobomatoso.
Subject(s)
Humans , Male , Female , Infant , Coloboma , Cysts , Microphthalmos , Orbital Neoplasms/congenital , Orbital Neoplasms/diagnosis , Diagnosis, DifferentialSubject(s)
Female , Follow-Up Studies , Humans , Infant , Male , Orbital Neoplasms/congenital , Teratoma/congenital , Tomography, X-Ray ComputedABSTRACT
En el presente trabajo, se estudiaron dos pacientes con baja visual progresiva, proptosis dinámica y deformidad orbitaria por masas tumorales retrooculares. El estudio oftalmológico condujo al diagnóstico de teratomas congénitos de la órbita en los dos casos clínicos. Se realizó evaluación y tratamiento en cada uno de ellos, con el subsecuente estudio de la historia natural de la enfermedad.
Subject(s)
Humans , Male , Female , Infant, Newborn , Teratoma/congenital , Teratoma/ultrastructure , Orbital Neoplasms/congenital , Orbital Neoplasms/physiopathology , Ultrasonography , Histology , Orbit/anatomy & histology , Orbit/physiopathologyABSTRACT
A case of congenital orbital teratoma with marked unilateral proptosis was noted at birth, Patients with congenital orbital teratoma had a uniform clinical picture and were very similar in their morphological pattern, often polycystic and with varied amounts of solid tissue. Six months after birth, the orbital tissues were totally extirpated. Histological examination revealed components from all three germinal layers and no sign of malignancy. Within the first year, the condition of the patient has been satisfactory.